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DeCS
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Descriptor English:
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Neoplastic Syndromes, Hereditary
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Descriptor Spanish:
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Síndromes Neoplásicos Hereditarios
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Descriptor Portuguese:
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Síndromes Neoplásicas Hereditárias
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Synonyms English:
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Cancer Syndrome, Hereditary
Cancer Syndromes, Hereditary
Hereditary Cancer Syndrome
Hereditary Cancer Syndromes
Hereditary Neoplastic Syndrome
Hereditary Neoplastic Syndromes
Neoplastic Syndrome, Hereditary
Syndrome, Hereditary Cancer
Syndrome, Hereditary Neoplastic
Syndromes, Hereditary Cancer
Syndromes, Hereditary Neoplastic
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Tree Number:
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C04.700
C16.320.700
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Definition English:
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The condition of a pattern of malignancies within a family, but not every individual's necessarily having the same neoplasm. Characteristically the tumor tends to occur at an earlier than average age, individuals may have more than one primary tumor, the tumors may be multicentric, usually more than 25 percent of the individuals in direct lineal descent from the proband are affected, and the cancer predisposition in these families behaves as an autosomal dominant trait with about 60 percent penetrance. |
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Indexing Annotation English:
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coordinate with specific hereditary organ/neoplasm term or specific hereditary histological type
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History Note English:
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87
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Allowable Qualifiers English:
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Record Number:
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19258
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Unique Identifier:
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D009386
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Occurrence in VHL:
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Similar:
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DeCS
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